Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(D8418) Other specified defect in the complement system 114
OUTPAT OUTPAT_ICD10(D849) Immunodeficiency, unspecified 87
OUTPAT OUTPAT_ICD10(D841) Defects in the complement system 66
OUTPAT OUTPAT_ICD10(D8419) Unspecified defect in the complement system 58
OUTPAT OUTPAT_ICD10(D848) Other specified immunodeficiencies 39
OUTPAT OUTPAT_ICD10(D8411) Hereditary angioedema type I 36
OUTPAT OUTPAT_ICD10(D8413) Hereditary angioedema type III 33
INPAT INPAT_ICD10(D849) Immunodeficiency, unspecified 30
INPAT INPAT_ICD10(D8418) Other specified defect in the complement system 26
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D849) Immunodeficiency, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 26
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D8418) Other specified defect in the complement system. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 25
INPAT INPAT_ICD10(D840) Lymphocyte function antigen-1 [LFA-1] defect 19
OUTPAT OUTPAT_ICD10(D840) Lymphocyte function antigen-1 [LFA-1] defect 19
INPAT INPAT_ICD10(D8413) Hereditary angioedema type III 17
OUTPAT OUTPAT_ICD10(D8412) Hereditary angioedema type II 15
INPAT INPAT_ICD10(D841) Defects in the complement system 13
INPAT INPAT_ICD10(D848) Other specified immunodeficiencies 13
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D8413) Hereditary angioedema type III. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 13
INPAT INPAT_ICD10(D8411) Hereditary angioedema type I 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D841) Defects in the complement system. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D848) Other specified immunodeficiencies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D8411) Hereditary angioedema type I. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 10
INPAT INPAT_ICD10(D8419) Unspecified defect in the complement system 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D84) Other immunodeficiencies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
OUTPAT OUTPAT_ICD10(D8414) C1 esterase inhibitor deficiency (C1-INH deficiency) 6
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D8419) Unspecified defect in the complement system. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5