Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(E752) Other sphingolipidosis 61
INPAT INPAT_ICD10(E752) Other sphingolipidosis 26
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(E752) Other sphingolipidosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 17
OUTPAT OUTPAT_ICD10(E755) Other lipid storage disorders 15
OUTPAT OUTPAT_ICD10(E756) Lipid storage disorder, unspecified 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(E756) Lipid storage disorder, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 10
INPAT INPAT_ICD10(E756) Lipid storage disorder, unspecified 9
OUTPAT OUTPAT_ICD10(E750) GM2gangliosidosis 7
OUTPAT OUTPAT_ICD10(E751) Other gangliosidosis 7
INPAT INPAT_ICD10(E755) Other lipid storage disorders 6
OUTPAT OUTPAT_ICD10(E753) Sphingolipidosis, unspecified 5
OUTPAT OUTPAT_ICD10(E754) Neuronal ceroid lipofuscinosis 5