Source Code Name Case count Share of cases (%)
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M353) Polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 4881
OUTPAT OUTPAT_ICD10(M353) Polymyalgia rheumatica 4340
OUTPAT OUTPAT_ICD10(M350) Sicca syndrome [Sjögren] 3160
INPAT INPAT_ICD10(M353) Polymyalgia rheumatica 2313
OUTPAT OUTPAT_ICD10(M357) Hypermobility syndrome 1993
OUTPAT OUTPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 1778
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M350) Sicca syndrome [Sjögren]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 1641
OUTPAT OUTPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 1163
OUTPAT OUTPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 1035
INPAT INPAT_ICD10(M350) Sicca syndrome [Sjögren] 1028
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M357) Hypermobility syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 753
INPAT INPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 682
OUTPAT OUTPAT_ICD10(M351) Other overlap syndromes 640
OUTPAT OUTPAT_ICD10(M313) Wegener's granulomatosis 537
OUTPAT OUTPAT_ICD10(M341) CR(E)ST syndrome 527
INPAT INPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 520
INPAT INPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 474
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 437
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M329) Systemic lupus erythematosus, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 429
INPAT INPAT_ICD10(M357) Hypermobility syndrome 394
INPAT INPAT_ICD10(M313) Wegener's granulomatosis 376
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M359) Systemic involvement of connective tissue, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 368
OUTPAT OUTPAT_ICD10(M349) Systemic sclerosis, unspecified 352
OUTPAT OUTPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 298
OUTPAT OUTPAT_ICD10(M328) Other forms of systemic lupus erythematosus 283
OUTPAT OUTPAT_ICD10(M316) Other giant cell arteritis 262
OUTPAT OUTPAT_ICD10(M332) Polymyositis 251
OUTPAT OUTPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 235
INPAT INPAT_ICD10(M351) Other overlap syndromes 225
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M341) CR(E)ST syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 220
OUTPAT OUTPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 207
OUTPAT OUTPAT_ICD10(M358) Other specified systemic involvement of connective tissue 198
INPAT INPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 191
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M313) Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 191
OUTPAT OUTPAT_ICD10(M355) Multifocal fibrosclerosis 185
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M351) Other overlap syndromes. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 184
INPAT INPAT_ICD9(7100A) Systemic lupus erythematosus 181
OUTPAT OUTPAT_ICD10(M317) Microscopic polyangiitis 181
INPAT INPAT_ICD10(M341) CR(E)ST syndrome 172
OUTPAT OUTPAT_ICD10(M311) Thrombotic microangiopathy 163
OUTPAT OUTPAT_ICD10(M300) Polyarteritis nodosa 159
OUTPAT OUTPAT_ICD10(M339) Dermatopolymyositis, unspecified 159
OUTPAT OUTPAT_ICD10(M331) Other dermatomyositis 151
OUTPAT OUTPAT_ICD10(M340) Progressive systemic sclerosis 148
INPAT INPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 142
INPAT INPAT_ICD10(M332) Polymyositis 142
INPAT INPAT_ICD10(M316) Other giant cell arteritis 134
OUTPAT OUTPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 127
OUTPAT OUTPAT_ICD10(M310) Hypersensitivity angiitis 127
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M32) Systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 125
OUTPAT OUTPAT_ICD10(M318) Other specified necrotizing vasculopathies 120
INPAT INPAT_ICD10(M300) Polyarteritis nodosa 117
INPAT INPAT_ICD10(M317) Microscopic polyangiitis 115
INPAT INPAT_ICD10(M349) Systemic sclerosis, unspecified 113
INPAT INPAT_ICD9(7250A) Polymyalgia rheumatica 113
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M349) Systemic sclerosis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 113
OUTPAT OUTPAT_ICD10(M348) Other forms of systemic sclerosis 109
INPAT INPAT_ICD10(M328) Other forms of systemic lupus erythematosus 104
INPAT INPAT_ICD10(M311) Thrombotic microangiopathy 102
OUTPAT OUTPAT_ICD10(M352) Behçet's disease 97
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M316) Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 95
INPAT INPAT_ICD9(7102B) Diffuse diseases of connective tissue, Sicca syndrome 94
INPAT INPAT_ICD10(M339) Dermatopolymyositis, unspecified 93
INPAT INPAT_ICD8(73491) Diffuse diseases of connective tissue, Collagenosis NUD 89
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M332) Polymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 86
INPAT INPAT_ICD9(7109X) Unspecified diffuse connective tissue disease 85
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M328) Other forms of systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 81
INPAT INPAT_ICD10(M310) Hypersensitivity angiitis 79
INPAT INPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 73
INPAT INPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 71
INPAT INPAT_ICD9(7102A) Diffuse diseases of connective tissue, Sicca syndrome 69
INPAT INPAT_ICD10(M318) Other specified necrotizing vasculopathies 67
INPAT INPAT_ICD10(M331) Other dermatomyositis 67
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M35) Other systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 67
OUTPAT OUTPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 66
OUTPAT OUTPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 65
OUTPAT OUTPAT_ICD10(M32) Systemic lupus erythematosus 64
INPAT INPAT_ICD10(M340) Progressive systemic sclerosis 62
INPAT INPAT_ICD10(M355) Multifocal fibrosclerosis 61
INPAT INPAT_ICD9(4476A) Arteritis, unspecified 61
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M321) Systemic lupus erythematosus with organ or system involvement. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 54
INPAT INPAT_ICD10(M348) Other forms of systemic sclerosis 51
INPAT INPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 50
OUTPAT OUTPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 50
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M358) Other specified systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 50
OUTPAT OUTPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 47
INPAT INPAT_ICD10(M358) Other specified systemic involvement of connective tissue 45
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M317) Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 44
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M339) Dermatopolymyositis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 44
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M34) Systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 44
INPAT INPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 42
OUTPAT OUTPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 40
OUTPAT OUTPAT_ICD10(M330) Juvenile dermatomyositis 38
DEATH DEATH_ICD10(M353) Polymyalgia rheumatica 37
INPAT INPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 36
INPAT INPAT_ICD10(M352) Behçet's disease 36
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M331) Other dermatomyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 36
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M348) Other forms of systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 36
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M319) Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 35
INPAT INPAT_ICD9(7108X) Other specified diffuse diseases of connective tissue 34
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 34
DEATH DEATH_ICD10(M313) Wegener's granulomatosis 33
INPAT INPAT_ICD8(44698) Polyarteritis nodosa and allied conditions, Other 33
INPAT INPAT_ICD8(73490) Diffuse diseases of connective tissue, Keratoconjunctivitis sicca (dry eye disease). Sjögren's syndrome 33
OUTPAT OUTPAT_ICD10(M35) Other systemic involvement of connective tissue 32
OUTPAT OUTPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 30
INPAT INPAT_ICD9(4461A) Acute febrile mucocutaneous lymph node syndrome [MCLS] 29
OUTPAT OUTPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 29
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M300) Polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 29
INPAT INPAT_ICD9(4462A) Hypersensitivity angiitis 28
INPAT INPAT_ICD9(4465A) Giant cell arteritis 26
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M352) Behçet's disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 26
INPAT INPAT_ICD9(7101A) Diffuse diseases of connective tissue, Systemic sclerosis 25
INPAT INPAT_ICD8(73498) Diffuse diseases of connective tissue, Alii definiti 24
INPAT INPAT_ICD9(4464A) Wegener's granulomatosis 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M314) Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
INPAT INPAT_ICD10(M330) Juvenile dermatomyositis 22
INPAT INPAT_ICD8(73499) Diffuse diseases of connective tissue, Other and unspecified 22
INPAT INPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 21
INPAT INPAT_ICD8(71610) Polymyositis and dermatomyositis, Polymyositis 21
INPAT INPAT_ICD9(7104A) Polymyositis 21
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M340) Progressive systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 21
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M354) Diffuse (eosinophilic) fasciitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 21
INPAT INPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 20
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M355) Multifocal fibrosclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 20
DEATH DEATH_ICD10(M341) CR(E)ST syndrome 19
DEATH DEATH_ICD10(M329) Systemic lupus erythematosus, unspecified 18
INPAT INPAT_ICD8(44638) Polyarteritis nodosa and allied conditions, Polymyalgia arteritica (rheumatica) 18
INPAT INPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 17
DEATH DEATH_ICD10(M350) Sicca syndrome [Sjögren] 16
INPAT INPAT_ICD9(4460A) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 16
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M318) Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 16
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 16
OUTPAT OUTPAT_ICD10(M312) Lethal midline granuloma 15
DEATH DEATH_ICD10(M317) Microscopic polyangiitis 14
DEATH DEATH_ICD10(M332) Polymyositis 14
INPAT INPAT_ICD8(71600) Polymyositis and dermatomyositis, Dermatomyositis 14
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M30) Polyarteritis nodosa and related conditions. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 14
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M310) Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 14
INPAT INPAT_ICD8(44600) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 13
INPAT INPAT_ICD9(7103B) Diffuse diseases of connective tissue, Dermatomyositis 13
OUTPAT OUTPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 13
DEATH DEATH_ICD10(M359) Systemic involvement of connective tissue, unspecified 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M308) Other conditions related to polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M33) Dermatopolymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
INPAT INPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 11
INPAT INPAT_ICD8(73409) Diffuse diseases of connective tissue, Sclerosis systematica NUD 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M311) Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
INPAT INPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 10
OUTPAT OUTPAT_ICD10(M34) Systemic sclerosis 10
OUTPAT OUTPAT_ICD10(M356) Relapsing panniculitis [Weber-Christian] 10
INPAT INPAT_ICD8(44630) Polyarteritis nodosa and allied conditions, Arteritis cranialis (temporalis) 9
INPAT INPAT_ICD9(4467A) Takayasu's disease 9
DEATH DEATH_ICD10(M351) Other overlap syndromes 8
INPAT INPAT_ICD9(4466A) Thrombotic microangiopathy 8
INPAT INPAT_ICD9(7103A) Diffuse diseases of connective tissue, Dermatomyositis 8
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M362) Haemophilic arthropathy (D66-D68+). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
DEATH DEATH_ICD10(M300) Polyarteritis nodosa 7
DEATH DEATH_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 7
DEATH DEATH_ICD10(M331) Other dermatomyositis 7
INPAT INPAT_ICD8(73401) Diffuse diseases of connective tissue, Sclerosis systematica acrosclerotica 7
INPAT INPAT_ICD8(74310) Other congenital anomalies of nervous system, Microcephalus 7
OUTPAT OUTPAT_ICD10(M342) Systemic sclerosis induced by drugs and chemicals 7
OUTPAT OUTPAT_ICD10(M360) Dermato(poly)myositis in neoplastic disease (C00-D48+) 7
DEATH DEATH_ICD10(M319) Necrotizing vasculopathy, unspecified 6
INPAT INPAT_ICD10(M312) Lethal midline granuloma 6
INPAT INPAT_ICD8(44620) Polyarteritis nodosa and allied conditions, Other hypersensitivity angiitis 6
INPAT INPAT_ICD9(4460B) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 6
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M320) Drug-induced systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 6
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M330) Juvenile dermatomyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 6
DEATH DEATH_ICD10(M311) Thrombotic microangiopathy 5
DEATH DEATH_ICD10(M316) Other giant cell arteritis 5
DEATH DEATH_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 5
DEATH DEATH_ICD10(M349) Systemic sclerosis, unspecified 5