| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M353) | Polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 5725 | |
| OUTPAT | OUTPAT_ICD10(M353) | Polymyalgia rheumatica | 4730 | |
| OUTPAT | OUTPAT_ICD10(M350) | Sicca syndrome [Sjögren] | 3259 | |
| INPAT | INPAT_ICD10(M353) | Polymyalgia rheumatica | 2615 | |
| OUTPAT | OUTPAT_ICD10(M357) | Hypermobility syndrome | 2046 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M350) | Sicca syndrome [Sjögren]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 1843 | |
| OUTPAT | OUTPAT_ICD10(M359) | Systemic involvement of connective tissue, unspecified | 1823 | |
| OUTPAT | OUTPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 1257 | |
| INPAT | INPAT_ICD10(M350) | Sicca syndrome [Sjögren] | 1105 | |
| OUTPAT | OUTPAT_ICD10(M329) | Systemic lupus erythematosus, unspecified | 1064 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M357) | Hypermobility syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 936 | |
| INPAT | INPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 737 | |
| OUTPAT | OUTPAT_ICD10(M351) | Other overlap syndromes | 648 | |
| OUTPAT | OUTPAT_ICD10(M341) | CR(E)ST syndrome | 561 | |
| OUTPAT | OUTPAT_ICD10(M313) | Wegener's granulomatosis | 548 | |
| INPAT | INPAT_ICD10(M329) | Systemic lupus erythematosus, unspecified | 546 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 522 | |
| INPAT | INPAT_ICD10(M359) | Systemic involvement of connective tissue, unspecified | 500 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M329) | Systemic lupus erythematosus, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 489 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M359) | Systemic involvement of connective tissue, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 444 | |
| INPAT | INPAT_ICD10(M357) | Hypermobility syndrome | 407 | |
| INPAT | INPAT_ICD10(M313) | Wegener's granulomatosis | 386 | |
| OUTPAT | OUTPAT_ICD10(M349) | Systemic sclerosis, unspecified | 359 | |
| OUTPAT | OUTPAT_ICD10(M316) | Other giant cell arteritis | 319 | |
| OUTPAT | OUTPAT_ICD10(M321) | Systemic lupus erythematosus with organ or system involvement | 305 | |
| OUTPAT | OUTPAT_ICD10(M328) | Other forms of systemic lupus erythematosus | 292 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M341) | CR(E)ST syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 264 | |
| OUTPAT | OUTPAT_ICD10(M332) | Polymyositis | 254 | |
| OUTPAT | OUTPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 246 | |
| INPAT | INPAT_ICD10(M351) | Other overlap syndromes | 235 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M313) | Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 214 | |
| OUTPAT | OUTPAT_ICD10(M358) | Other specified systemic involvement of connective tissue | 213 | |
| OUTPAT | OUTPAT_ICD10(M320) | Drug-induced systemic lupus erythematosus | 210 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M351) | Other overlap syndromes. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 206 | |
| OUTPAT | OUTPAT_ICD10(M317) | Microscopic polyangiitis | 200 | |
| INPAT | INPAT_ICD10(M321) | Systemic lupus erythematosus with organ or system involvement | 196 | |
| INPAT | INPAT_ICD10(M341) | CR(E)ST syndrome | 192 | |
| OUTPAT | OUTPAT_ICD10(M355) | Multifocal fibrosclerosis | 188 | |
| INPAT | INPAT_ICD9(7100A) | Systemic lupus erythematosus | 181 | |
| OUTPAT | OUTPAT_ICD10(M311) | Thrombotic microangiopathy | 171 | |
| OUTPAT | OUTPAT_ICD10(M300) | Polyarteritis nodosa | 168 | |
| OUTPAT | OUTPAT_ICD10(M339) | Dermatopolymyositis, unspecified | 168 | |
| INPAT | INPAT_ICD10(M316) | Other giant cell arteritis | 160 | |
| OUTPAT | OUTPAT_ICD10(M331) | Other dermatomyositis | 154 | |
| OUTPAT | OUTPAT_ICD10(M340) | Progressive systemic sclerosis | 152 | |
| INPAT | INPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 148 | |
| INPAT | INPAT_ICD10(M332) | Polymyositis | 145 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M32) | Systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 138 | |
| INPAT | INPAT_ICD10(M317) | Microscopic polyangiitis | 134 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M349) | Systemic sclerosis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 133 | |
| OUTPAT | OUTPAT_ICD10(M301) | Polyarteritis with lung involvement [Churg-Strauss] | 132 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M316) | Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 132 | |
| OUTPAT | OUTPAT_ICD10(M310) | Hypersensitivity angiitis | 129 | |
| OUTPAT | OUTPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 125 | |
| INPAT | INPAT_ICD10(M300) | Polyarteritis nodosa | 122 | |
| INPAT | INPAT_ICD10(M349) | Systemic sclerosis, unspecified | 117 | |
| OUTPAT | OUTPAT_ICD10(M348) | Other forms of systemic sclerosis | 116 | |
| INPAT | INPAT_ICD9(7250A) | Polymyalgia rheumatica | 113 | |
| INPAT | INPAT_ICD10(M328) | Other forms of systemic lupus erythematosus | 108 | |
| INPAT | INPAT_ICD10(M311) | Thrombotic microangiopathy | 107 | |
| OUTPAT | OUTPAT_ICD10(M352) | Behçet's disease | 98 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M328) | Other forms of systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 98 | |
| INPAT | INPAT_ICD10(M339) | Dermatopolymyositis, unspecified | 97 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M332) | Polymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 97 | |
| INPAT | INPAT_ICD9(7102B) | Diffuse diseases of connective tissue, Sicca syndrome | 94 | |
| INPAT | INPAT_ICD8(73491) | Diffuse diseases of connective tissue, Collagenosis NUD | 89 | |
| INPAT | INPAT_ICD9(7109X) | Unspecified diffuse connective tissue disease | 85 | |
| INPAT | INPAT_ICD10(M310) | Hypersensitivity angiitis | 83 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M35) | Other systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 82 | |
| INPAT | INPAT_ICD10(M301) | Polyarteritis with lung involvement [Churg-Strauss] | 76 | |
| INPAT | INPAT_ICD10(M320) | Drug-induced systemic lupus erythematosus | 73 | |
| INPAT | INPAT_ICD10(M331) | Other dermatomyositis | 70 | |
| INPAT | INPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 69 | |
| INPAT | INPAT_ICD9(7102A) | Diffuse diseases of connective tissue, Sicca syndrome | 69 | |
| OUTPAT | OUTPAT_ICD10(M308) | Other conditions related to polyarteritis nodosa | 68 | |
| OUTPAT | OUTPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 67 | |
| OUTPAT | OUTPAT_ICD10(M32) | Systemic lupus erythematosus | 67 | |
| INPAT | INPAT_ICD10(M340) | Progressive systemic sclerosis | 63 | |
| INPAT | INPAT_ICD10(M355) | Multifocal fibrosclerosis | 62 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M321) | Systemic lupus erythematosus with organ or system involvement. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 62 | |
| INPAT | INPAT_ICD9(4476A) | Arteritis, unspecified | 61 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M358) | Other specified systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 60 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M317) | Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 57 | |
| INPAT | INPAT_ICD10(M348) | Other forms of systemic sclerosis | 56 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M339) | Dermatopolymyositis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 54 | |
| INPAT | INPAT_ICD10(M358) | Other specified systemic involvement of connective tissue | 53 | |
| DEATH | DEATH_ICD10(M353) | Polymyalgia rheumatica | 51 | |
| OUTPAT | OUTPAT_ICD10(M354) | Diffuse (eosinophilic) fasciitis | 51 | |
| INPAT | INPAT_ICD10(M308) | Other conditions related to polyarteritis nodosa | 50 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M34) | Systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 49 | |
| OUTPAT | OUTPAT_ICD10(M303) | Mucocutaneous lymph node syndrome [Kawasaki] | 48 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M348) | Other forms of systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 45 | |
| DEATH | DEATH_ICD10(M313) | Wegener's granulomatosis | 44 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M331) | Other dermatomyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 44 | |
| INPAT | INPAT_ICD10(M303) | Mucocutaneous lymph node syndrome [Kawasaki] | 43 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M319) | Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 42 | |
| OUTPAT | OUTPAT_ICD10(M364) | Arthropathy in hypersensitivity reactions classified elsewhere | 41 | |
| OUTPAT | OUTPAT_ICD10(M330) | Juvenile dermatomyositis | 37 | |
| INPAT | INPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 36 | |
| INPAT | INPAT_ICD10(M352) | Behçet's disease | 35 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M300) | Polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 35 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M301) | Polyarteritis with lung involvement [Churg-Strauss]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 35 | |
| INPAT | INPAT_ICD9(7108X) | Other specified diffuse diseases of connective tissue | 34 | |
| INPAT | INPAT_ICD8(44698) | Polyarteritis nodosa and allied conditions, Other | 33 | |
| INPAT | INPAT_ICD8(73490) | Diffuse diseases of connective tissue, Keratoconjunctivitis sicca (dry eye disease). Sjögren's syndrome | 33 | |
| OUTPAT | OUTPAT_ICD10(M35) | Other systemic involvement of connective tissue | 33 | |
| OUTPAT | OUTPAT_ICD10(M362) | Haemophilic arthropathy (D66-D68+) | 30 | |
| OUTPAT | OUTPAT_ICD10(M368) | Systemic disorders of connective tissue in other diseases classified elsewhere | 30 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M340) | Progressive systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 30 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M352) | Behçet's disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 30 | |
| INPAT | INPAT_ICD9(4461A) | Acute febrile mucocutaneous lymph node syndrome [MCLS] | 29 | |
| INPAT | INPAT_ICD9(4462A) | Hypersensitivity angiitis | 28 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M355) | Multifocal fibrosclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 28 | |
| DEATH | DEATH_ICD10(M341) | CR(E)ST syndrome | 26 | |
| INPAT | INPAT_ICD9(4465A) | Giant cell arteritis | 26 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M314) | Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 26 | |
| INPAT | INPAT_ICD9(7101A) | Diffuse diseases of connective tissue, Systemic sclerosis | 25 | |
| INPAT | INPAT_ICD8(73498) | Diffuse diseases of connective tissue, Alii definiti | 24 | |
| INPAT | INPAT_ICD9(4464A) | Wegener's granulomatosis | 24 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M354) | Diffuse (eosinophilic) fasciitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 23 | |
| DEATH | DEATH_ICD10(M329) | Systemic lupus erythematosus, unspecified | 22 | |
| DEATH | DEATH_ICD10(M350) | Sicca syndrome [Sjögren] | 22 | |
| INPAT | INPAT_ICD8(73499) | Diffuse diseases of connective tissue, Other and unspecified | 22 | |
| DEATH | DEATH_ICD10(M317) | Microscopic polyangiitis | 21 | |
| INPAT | INPAT_ICD10(M330) | Juvenile dermatomyositis | 21 | |
| INPAT | INPAT_ICD10(M354) | Diffuse (eosinophilic) fasciitis | 21 | |
| INPAT | INPAT_ICD10(M364) | Arthropathy in hypersensitivity reactions classified elsewhere | 21 | |
| INPAT | INPAT_ICD8(71610) | Polymyositis and dermatomyositis, Polymyositis | 21 | |
| INPAT | INPAT_ICD9(7104A) | Polymyositis | 21 | |
| INPAT | INPAT_ICD8(44638) | Polyarteritis nodosa and allied conditions, Polymyalgia arteritica (rheumatica) | 18 | |
| DEATH | DEATH_ICD10(M332) | Polymyositis | 17 | |
| INPAT | INPAT_ICD10(M362) | Haemophilic arthropathy (D66-D68+) | 17 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M318) | Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 17 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M364) | Arthropathy in hypersensitivity reactions classified elsewhere. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 17 | |
| INPAT | INPAT_ICD9(4460A) | Polyarteritis nodosa and allied conditions, Polyarteritis nodosa | 16 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M308) | Other conditions related to polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 16 | |
| DEATH | DEATH_ICD10(M359) | Systemic involvement of connective tissue, unspecified | 15 | |
| OUTPAT | OUTPAT_ICD10(M312) | Lethal midline granuloma | 15 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M30) | Polyarteritis nodosa and related conditions. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 15 | |
| INPAT | INPAT_ICD8(71600) | Polymyositis and dermatomyositis, Dermatomyositis | 14 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M310) | Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 14 | |
| INPAT | INPAT_ICD8(44600) | Polyarteritis nodosa and allied conditions, Polyarteritis nodosa | 13 | |
| INPAT | INPAT_ICD9(7103B) | Diffuse diseases of connective tissue, Dermatomyositis | 13 | |
| OUTPAT | OUTPAT_ICD10(M361) | Arthropathy in neoplastic disease (C00-D48+) | 13 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M311) | Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 13 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M33) | Dermatopolymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 12 | |
| DEATH | DEATH_ICD10(M321) | Systemic lupus erythematosus with organ or system involvement | 11 | |
| DEATH | DEATH_ICD10(M331) | Other dermatomyositis | 11 | |
| INPAT | INPAT_ICD10(M361) | Arthropathy in neoplastic disease (C00-D48+) | 11 | |
| INPAT | INPAT_ICD8(73409) | Diffuse diseases of connective tissue, Sclerosis systematica NUD | 11 | |
| OUTPAT | OUTPAT_ICD10(M34) | Systemic sclerosis | 11 | |
| OUTPAT | OUTPAT_ICD10(M356) | Relapsing panniculitis [Weber-Christian] | 11 | |
| DEATH | DEATH_ICD10(M300) | Polyarteritis nodosa | 10 | |
| DEATH | DEATH_ICD10(M351) | Other overlap syndromes | 10 | |
| INPAT | INPAT_ICD10(M368) | Systemic disorders of connective tissue in other diseases classified elsewhere | 10 | |
| INPAT | INPAT_ICD8(44630) | Polyarteritis nodosa and allied conditions, Arteritis cranialis (temporalis) | 9 | |
| INPAT | INPAT_ICD9(4467A) | Takayasu's disease | 9 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M362) | Haemophilic arthropathy (D66-D68+). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 9 | |
| DEATH | DEATH_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 8 | |
| DEATH | DEATH_ICD10(M348) | Other forms of systemic sclerosis | 8 | |
| INPAT | INPAT_ICD9(4466A) | Thrombotic microangiopathy | 8 | |
| INPAT | INPAT_ICD9(7103A) | Diffuse diseases of connective tissue, Dermatomyositis | 8 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M320) | Drug-induced systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 8 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M330) | Juvenile dermatomyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 8 | |
| DEATH | DEATH_ICD10(M311) | Thrombotic microangiopathy | 7 | |
| DEATH | DEATH_ICD10(M316) | Other giant cell arteritis | 7 | |
| DEATH | DEATH_ICD10(M349) | Systemic sclerosis, unspecified | 7 | |
| INPAT | INPAT_ICD8(73401) | Diffuse diseases of connective tissue, Sclerosis systematica acrosclerotica | 7 | |
| INPAT | INPAT_ICD8(74310) | Other congenital anomalies of nervous system, Microcephalus | 7 | |
| OUTPAT | OUTPAT_ICD10(M342) | Systemic sclerosis induced by drugs and chemicals | 7 | |
| OUTPAT | OUTPAT_ICD10(M360) | Dermato(poly)myositis in neoplastic disease (C00-D48+) | 7 | |
| DEATH | DEATH_ICD10(M319) | Necrotizing vasculopathy, unspecified | 6 | |
| INPAT | INPAT_ICD10(M312) | Lethal midline granuloma | 6 | |
| INPAT | INPAT_ICD8(44620) | Polyarteritis nodosa and allied conditions, Other hypersensitivity angiitis | 6 | |
| INPAT | INPAT_ICD9(4460B) | Polyarteritis nodosa and allied conditions, Polyarteritis nodosa | 6 | |
| DEATH | DEATH_ICD10(M301) | Polyarteritis with lung involvement [Churg-Strauss] | 5 | |
| DEATH | DEATH_ICD10(M340) | Progressive systemic sclerosis | 5 | |
| OUTPAT | OUTPAT_ICD10(M31) | Other necrotizing vasculopathies | 5 |