Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(Q8500) Neurofibromatosis, type 1 245
OUTPAT OUTPAT_ICD10(Q8509) Unspecified neurofibromatosis 161
INPAT INPAT_ICD10(Q8500) Neurofibromatosis, type 1 120
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8500) Neurofibromatosis, type 1. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 95
OUTPAT OUTPAT_ICD10(Q851) Tuberous sclerosis 74
OUTPAT OUTPAT_ICD10(Q8501) Neurofibromatosis, type 2 65
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q850) Neurofibromatosis (nonmalignant). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 64
INPAT INPAT_ICD10(Q8509) Unspecified neurofibromatosis 56
OUTPAT OUTPAT_ICD10(Q850) Neurofibromatosis (nonmalignant) 50
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8509) Unspecified neurofibromatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 43
INPAT INPAT_ICD10(Q851) Tuberous sclerosis 36
OUTPAT OUTPAT_ICD10(Q8582) of Hipple-Lindau syndrome 31
INPAT INPAT_ICD10(Q8501) Neurofibromatosis, type 2 27
OUTPAT OUTPAT_ICD10(Q859) Phakomatosis, unspecified 27
INPAT INPAT_ICD10(Q850) Neurofibromatosis (nonmalignant) 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q851) Tuberous sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 21
INPAT INPAT_ICD10(Q8582) of Hipple-Lindau syndrome 17
OUTPAT OUTPAT_ICD10(Q8580) Peutz-Jegher syndrome 15
OUTPAT OUTPAT_ICD10(Q8588) Other phakomatoses, not elsewhere classified 14
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8501) Neurofibromatosis, type 2. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 14
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8582) of Hipple-Lindau syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
OUTPAT OUTPAT_ICD10(Q8581) Sturge-Weber syndrome 10
INPAT INPAT_ICD10(Q859) Phakomatosis, unspecified 9
OUTPAT OUTPAT_ICD10(Q8583) Gardner syndrome 9
DEATH DEATH_ICD10(Q850) Neurofibromatosis (nonmalignant) 8
INPAT INPAT_ICD10(Q8580) Peutz-Jegher syndrome 8
INPAT INPAT_ICD10(Q8581) Sturge-Weber syndrome 8
INPAT INPAT_ICD10(Q8588) Other phakomatoses, not elsewhere classified 7
DEATH DEATH_ICD10(Q858) Name not found 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8581) Sturge-Weber syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5